Congenital Heart Disease A Clinical, Pathological, Embryological, and Segmental Analysis

Authored by the originator of the standard nomenclature for this spectrum of disorders, Congenital Heart Disease: A Clinical, Pathological, Embryological, and Segmental Analysis discusses the history, anatomic features, and physiologic consequences of CHD-in one authoritative resource. The Van Praagh approach to the segmental classification of CHD, developed and implemented by Dr. Richard Van Praagh in the 1960s at Boston Children’s Hospital, remains widely used today, facilitating communication among radiologists, cardiologists, surgeons, and pediatricians who are involved in the diagnosis, characterization, and management of this disease. This unique atlas offers complete coverage of the ubiquitous Van Praagh “language” of CHD, including the signs, symptoms, and clinical manifestations of malpositioned, malformed, or absent cardiovascular chambers, vessels, and valves using traditional as well as state-of-the-art technology.

Table of Contents

1 Brief History of the Cardiovascular System
2 Embryology and Etiology
2 Conclusions
2 Conclusions
2 Conclusions
2 Conclusions
2 Conclusions
3 Morphologic Anatomy
4 Segmental Anatomy
5 The Congenital Cardiac Pathology Database
6 Systemic Venous Anomalies
7 Pulmonary Venous Anomalies
8 Cor Triatriatum Sinistrum (Subdivided Left Atrium) and Cor Triatriatum Dextrum (Subdivided Right Atrium)
9 Interatrial Communications
10 Juxtaposition of the Atrial Appendages
11 Common Atrioventricular Canal
12 Double-Outlet and Common-Outlet Right Atrium
13 Tricuspid Valve Anomalies
14 Mitral Valve Anomalies
15 Infundibuloarterial Situs Equations: How Normally and Abnormally Related Great Arteries are Built and the Importance of Infundibuloarterial Situs Concordance and Discordance
16 Ventricular Septal Defects
17 Single Ventricle
18 Superoinferior Ventricles
19 Anomalous Ifundibular Muscle Bundles
20 Tetralogy of Fallot
21 Absence of the Subpulmonary Infundibulum with its Sequelae has been Misinterpreted as Common Aortopulmonary Trunk that Probably Does Not Exist
22 Transposition of the Great Arteries
23 Double-Outlet Right Ventricle
24 Double-Outlet Left Ventricle
25 Anatomically Corrected Malposition of the Great Arteries
26 What Prevents and What Permits the Embryonic Great Arterial Switch?
27 Infundibulo-Arterial Situs Equations and Analysis
28 The Cardiac Conduction System
29 The Heterotaxy Syndromes: Asplenia, Polysplenia, and with Normally Formed but Right-Sided Spleen
30 Conclusions
 Appendix